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presentamos un caso de displasia fibrosa monostótica localizada en el seno entre ellos el síndrome de albright (sólo en casos de displasia poliostótica). su. Displasia fibrosa monostótica e poliostótica. Front Cover. Simone Paula Bibliographic information. QR code for Displasia fibrosa monostótica e poliostótica. Download PDF. 1 / 3 Pages. Previous article. Go back to website. Next article.

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McCune Albright syndrome – diffuse orbital involvement due to fibrous dysplasia: a case report

In general, the lesion begins in the childhood and progresses during puberty, ceasing after adolescence 4. Leed e Seaman, emidentificaram o osso frontal e o esfenoidal como os mais comumente envolvidos 4.

Moreover, CT can be used to complement the diagnosis and improve the interpretation of MRI examinations of lesions in the bones of skull base and face, since the appearance of unpolished glass will confirm the diagnosis of FD.

Craniofacial fibrous dysplasia CFD of the maxilla in an year old boy: Unilateral blindness after ipsilateral prophylactic transcranial optic canal decompression for fibrous dysplasia. Fronto-orbital sphenoidal fibrous dysplasia.

Among these plliostotica, one can observe periosteal widening and bone sequestration in the osteomyelitis; characteristic periosteal reaction with sun-beams appearance, cortical destruction and widening of the periodontal ligament space 2 in the osteosarcoma 17 ; and ossifying fibroma with precise limits, smooth margins and concentric expansion 117 – In some cases in which FD causes neither painful symptoms 7 nor aesthetical problems, there is no need of surgical treatment 1710which is recommended when maxilla and mandible are both affected by the lesion 1 As the majority of the monostotic lesions are asymptomatic, they are only discovered by means of imaging examinations ordered for other purposes 13diaplasia Due to the unpolished glass appearance of FD on the images 13the imaging diagnosis is enough and thus bone biopsy is not necessary 8 Although some studies reported the indication of magnetic resonance imaging MRI for diagnosis of FD 62026this type of examination does not reveal the distinctive characteristic of FD as observed in radiographs and CT images monowtotica820since the lesion may often be confounded with tumours 6poliosgotica.


It is worth emphasising that although FD becomes stable after bone maturation 131517 – 19there are cases in which the lesion can be re-activated or activated during pregnancy, thus suggesting a possible influence of sexual hormones 212 The most common clinical symptom in the cases of craniofacial FD is a painless swelling in the region dispplasia, including facial asymmetry which may cause severe deformity resulting in functional and aesthetic compromise 6 The purpose of this study is poliostoticz make a review of the main clinical, radiological and histopathological findings that contributes to the differential diagnosis.

The increased familiarity with the imaging characteristics of fibrous dysplasia can assist the dentist-surgeon in the early diagnosis and treatment of patients. In the image exams, the main characteristic of fibrous dysplasia is its unpolished glass appearance.

Discrete invasion of the maxillary sinus was also observed, with the lateral wall being slightly expanded. Computed tomography of cranio-facial fibrous dysplasia. One can also observe that the mucosa covering the affected bone appears to be healthy and normal 10 It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. Fibrous dysplasia is a pseudo-neoplastic lesion, ethiology unknown, benign and recurrent, which normal bone is replaced by fibrous tissue and lamelar bone trabeculae.

Accuracy of linear measurements of Galileos cone beam computed tomography in normal and different head positions. In addition, because the patient was 10 years old, a follow-up by means of imaging examinations to be performed periodically was proposed in order to avoid possible relapse in the case of surgical treatment.

Monostotic fibrous dysplasia: a case report with cone-beam computed tomography findings

Int J Oral Maxillofac Surg. The surgical treatment of fibrous dysplasia. Fibrous dysplasia is a benign fibrous-osseous lesion in which normal bone is replaced by fibrous connective tissue and immature bone, affecting only one monostotic or several bones polyostotic and mainly occurring in children and young adults. FD is frequently found in children and young adults 617such as in the present case of a female year-old patient.

Reliability and reproducibility of linear mandible measurements with the use of a cone-beam computed tomography and two object inclinations.


The patient did not remember to have suffered any trauma on the region. In this way, CT is a definitive examination for early diagnosis, surgery planning and follow-up of patients. Artigo aceito em 20 de novembro de A year database CT imaging of craniofacial fibrous dysplasia.

All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. Therefore, the presence of bone expansion, thin cortex, well-defined borders and unpolished glass appearance 2 – 3691116 – 19 is observed on these images.

It is important to pay attention to the moment of surgery, since monostotic lesions tend to be inactivated after skeletal maturation, whereas the polyostotic ones remain active during the adult phase How to cite this article.

In all three cases, the diagnosis was confirmed based on histopathological findings.

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Therefore, the introduction of CBCT in dentistry also promoted its use for diagnosing FD 16 – 17 not only because of the advantages of less radiation dosage and less cost compared to CT, but also because of its better image quality for hard tissues 22 – The polyostotic form is rarer and mainly occurring in long bones 610 and possibly associated with McCune-Albright syndrome, which is characterised by the presence of coffee-milk cutaneous pigmentation and endocrinopathy 136 – 1016 Ann Otol Rhinol Laryngol ; In this type of FD, man and women are affected with the same frequency 712 – 13 According to Hanifi et al.

Imaging of craniofacial fibrous dysplasia. Fibrous dysplasia FD is a rare benign fibro-osseous lesion 1 – 7 characterised by the gradual replacement of the normal bone by fibrous tissue and immature bone 58.

Fibrous dysplasia in the maxilla: According to Lisle et al.

In addition, according to Assaf et al. Due to Fibrous Dysplasia and Ossifying Fibroma similar clinical courses, the histopathological findings are essential to their differential diagnosis.

According to Akintoye et al.